Eosinophilic Granulomatosis with Polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare vasculitis that often involves the respiratory tract, affects small to medium vessels, and is associated with asthma and eosinophilia. EGPA is difficult to diagnose and manage due to its rarity and complexity. Early recognition is critical to avoid organ damage. This educational session will review the pathogenesis, clinical manifestations, classification criteria, diagnosis and prognosis of EGPA.